. "La malattia di Caroli \u00E8 una patologia congenita che si caratterizza per la presenza di cisti dei dotti biliari intraepatici. Quest'evento sembra essere legato alla dilatazione segmentale e multifocale, ma non si conosce l'evento scatenante, esordisce in qualunque et\u00E0 con prevalenza nel sesso femminile e con carattere ereditario autosomico recessivo. \u00C8 una malattia molto rara e ad oggi sono stati descritti meno di trecento casi in tutto il mondo. Oltre alla dilatazione delle vie intraepatiche non sussistono altre alterazioni."@it . . "\u0421\u0438\u043D\u0434\u0440\u043E\u043C \u041A\u0430\u0440\u043E\u043B\u0438"@ru . "29874" . . . "\u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A (\u0628\u0627\u0644\u0625\u0646\u062C\u0644\u064A\u0632\u064A\u0629: Caroli disease)\u200F (\u062A\u0648\u0633\u0639 \u0643\u0647\u0641\u064A \u0645\u062A\u0635\u0644\u060C \u0623\u0648 \u062A\u0648\u0633\u0639 \u0643\u064A\u0633\u064A \u062E\u0644\u0642\u064A \u0644\u0644\u0623\u0642\u0646\u064A\u0629 \u0627\u0644\u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u062F\u0627\u062E\u0644 \u0627\u0644\u0643\u0628\u062F) \u0647\u0648 \u0627\u0636\u0637\u0631\u0627\u0628 \u0648\u0631\u0627\u062B\u064A \u0646\u0627\u062F\u0631 \u064A\u062A\u0645\u064A\u0632 \u0628\u0627\u0644\u062A\u0648\u0633\u0639 \u0627\u0644\u0643\u064A\u0633\u064A\u060C \u0623\u0648 \u062A\u0648\u0633\u0639 \u0627\u0644\u0642\u0646\u0648\u0627\u062A \u0627\u0644\u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u062F\u0627\u062E\u0644 \u0627\u0644\u0643\u0628\u062F. \u064A\u0648\u062C\u062F \u0646\u0645\u0637\u0627\u0646 \u0644\u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A: \u064A\u062A\u0643\u0648\u0646 \u062F\u0627\u0621 \u0643\u0627\u0631\u0648\u0644\u064A \u0627\u0644\u0628\u0624\u0631\u064A \u0623\u0648 \u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A \u0627\u0644\u0628\u0633\u064A\u0637 \u0645\u0646 \u0642\u0646\u0648\u0627\u062A \u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u0645\u062A\u0633\u0639\u0629 \u0628\u0634\u0643\u0644 \u063A\u064A\u0631 \u0637\u0628\u064A\u0639\u064A \u062A\u0624\u062B\u0631 \u0639\u0644\u0649 \u062C\u0632\u0621 \u0645\u0639\u0632\u0648\u0644 \u0645\u0646 \u0627\u0644\u0643\u0628\u062F. \u0627\u0644\u0634\u0643\u0644 \u0627\u0644\u062B\u0627\u0646\u064A \u0623\u0643\u062B\u0631 \u0627\u0646\u062A\u0634\u0627\u0631\u064B\u0627\u060C \u0648\u0639\u0646\u062F\u0645\u0627 \u064A\u0631\u062A\u0628\u0637 \u0628\u0627\u0631\u062A\u0641\u0627\u0639 \u0636\u063A\u0637 \u0627\u0644\u062F\u0645 \u0627\u0644\u0628\u0627\u0628\u064A \u0648\u0627\u0644\u062A\u0644\u064A\u0641 \u0627\u0644\u0643\u0628\u062F\u064A \u0627\u0644\u062E\u0644\u0642\u064A \u063A\u0627\u0644\u0628\u064B\u0627 \u0645\u0627 \u064A\u0634\u0627\u0631 \u0625\u0644\u064A\u0647 \u0628\u0627\u0633\u0645 \u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0643\u0627\u0631\u0648\u0644\u064A. \u0627\u0644\u0627\u062E\u062A\u0644\u0627\u0641\u0627\u062A \u0627\u0644\u0623\u0633\u0627\u0633\u064A\u0629 \u0628\u064A\u0646 \u0627\u0644\u0646\u0648\u0639\u064A\u0646 \u0644\u064A\u0633\u062A \u0645\u0641\u0647\u0648\u0645\u0629 \u062C\u064A\u062F\u064B\u0627. \u064A\u0631\u062A\u0628\u0637 \u062F\u0627\u0621 \u0643\u0627\u0631\u0648\u0644\u064A \u0623\u064A\u0636\u064B\u0627 \u0628\u0641\u0634\u0644 \u0627\u0644\u0643\u0628\u062F \u0648\u062F\u0627\u0621 \u0627\u0644\u0643\u0644\u0649 \u0645\u062A\u0639\u062F\u062F \u0627\u0644\u0643\u064A\u0633\u0627\u062A. \u064A\u0635\u064A\u0628 \u0627\u0644\u0645\u0631\u0636 \u0634\u062E\u0635\u064B\u0627 \u0648\u0627\u062D\u062F\u064B\u0627 \u0645\u0646 \u0628\u064A\u0646 \u0643\u0644 \u0645\u0644\u064A\u0648\u0646 \u0634\u062E\u0635\u060C \u0645\u0639 \u0648\u062C\u0648\u062F \u062D\u0627\u0644\u0627\u062A \u0625\u0635\u0627\u0628\u0629 \u0628\u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0643\u0627\u0631\u0648\u0644\u064A \u0623\u0643\u062B\u0631 \u0645\u0646 \u0627\u0644\u0645\u0631\u0636. \u064A\u062E\u062A\u0644\u0641 \u062F\u0627\u0621 \u0643\u0627\u0631\u0648\u0644\u064A \u0639\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0623\u062E\u0631\u0649 \u0627\u0644\u062A\u064A \u062A\u0633\u0628\u0628 \u062A\u0648\u0633\u0639 \u0627\u0644\u0623\u0642\u0646\u064A\u0629 \u0627\u0644\u0646\u0627\u062C\u0645 \u0639\u0646 \u0627\u0644\u0627\u0646\u0633\u062F\u0627\u062F\u060C \u0625\u0630 \u0623\u0646\u0647 \u0644\u064A\u0633 \u0623\u062D\u062F \u0645\u0634\u062A\u0642\u0627\u062A \u0627\u0644\u0643\u064A\u0633 \u0627\u0644\u0635\u0641\u0631\u0627\u0648\u064A \u0627\u0644\u0645\u062A\u0639\u062F\u062F."@ar . . . . . . . "263200"^^ . . . . . . . . . "Caroli disease"@en . . . . . . . . . . . . . . "D016767" . "717232005"^^ . . "131"@en . . . . . . . . . . . . "Caroli disease (communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree) is a rare inherited disorder characterized by cystic dilatation (or ectasia) of the bile ducts within the liver. There are two patterns of Caroli disease: focal or simple Caroli disease consists of abnormally widened bile ducts affecting an isolated portion of liver. The second form is more diffuse, and when associated with portal hypertension and congenital hepatic fibrosis, is often referred to as \"Caroli syndrome\". The underlying differences between the two types are not well understood. Caroli disease is also associated with liver failure and polycystic kidney disease. The disease affects about one in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease. Caroli disease is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many choledochal cyst derivatives."@en . "Das Caroli-Syndrom, benannt nach seinem Erstbeschreiber Jacques Caroli (1902\u20131979), ist eine seltene angeborene Erkrankung der Gallenwege mit zystischen Erweiterungen der Galleng\u00E4nge in Kombination mit einer angeborenen Fibrose der Leber. Die isolierte Erweiterung der gro\u00DFen Gallenwege ohne Bindegewebsvermehrung ist als Caroli-Krankheit bekannt."@de . . . . "Enfermedad de Caroli"@es . . . . . "Doen\u00E7a de Caroli \u00E9 um dist\u00FArbio heredit\u00E1rio raro caracterizado por dilata\u00E7\u00E3o c\u00EDstica (ou ectasia) dos ductos biliares no f\u00EDgado. Existem dois padr\u00F5es de doen\u00E7a de Caroli: a doen\u00E7a focal ou simples consiste em ductos biliares anormalmente alargados que afetam uma por\u00E7\u00E3o isolada do f\u00EDgado. A segunda forma \u00E9 mais difusa e, quando associada \u00E0 hipertens\u00E3o portal e , \u00E9 frequentemente chamada de \"s\u00EDndrome de Caroli\". As diferen\u00E7as subjacentes entre os dois tipos n\u00E3o s\u00E3o bem compreendidas. Tamb\u00E9m est\u00E1 associada a insufici\u00EAncia hep\u00E1tica e doen\u00E7a renal polic\u00EDstica. A doen\u00E7a afeta cerca de uma em 1 milh\u00E3o de pessoas, com mais casos relatados de s\u00EDndrome de Caroli do que de doen\u00E7a de Caroli."@pt . "La Enfermedad de Caroli (ectasia cavernosa comunicante o dilataci\u00F3n qu\u00EDstica cong\u00E9nita del \u00E1rbol biliar intrahep\u00E1tico ) es un raro desorden hereditario caracterizado por la dilataci\u00F3n de los ductos biliares intrahep\u00E1ticos. Se consideran dos subtipos de enfermedad de Caroli, siendo el m\u00E1s frecuente el llamado simple o aislado y se presenta cuando los ductos biliares se encuentran dilatados por ectasia. El segundo subtipo, m\u00E1s complejo, se conoce com\u00FAnmente como s\u00EDndrome de Caroli. Esta forma compleja se encuentra vinculada a hipertensi\u00F3n portal y .\u200B"@es . . . . "12403"^^ . . . . . . . . . "Doen\u00E7a de Caroli \u00E9 um dist\u00FArbio heredit\u00E1rio raro caracterizado por dilata\u00E7\u00E3o c\u00EDstica (ou ectasia) dos ductos biliares no f\u00EDgado. Existem dois padr\u00F5es de doen\u00E7a de Caroli: a doen\u00E7a focal ou simples consiste em ductos biliares anormalmente alargados que afetam uma por\u00E7\u00E3o isolada do f\u00EDgado. A segunda forma \u00E9 mais difusa e, quando associada \u00E0 hipertens\u00E3o portal e , \u00E9 frequentemente chamada de \"s\u00EDndrome de Caroli\". As diferen\u00E7as subjacentes entre os dois tipos n\u00E3o s\u00E3o bem compreendidas. Tamb\u00E9m est\u00E1 associada a insufici\u00EAncia hep\u00E1tica e doen\u00E7a renal polic\u00EDstica. A doen\u00E7a afeta cerca de uma em 1 milh\u00E3o de pessoas, com mais casos relatados de s\u00EDndrome de Caroli do que de doen\u00E7a de Caroli. \u00C9 distinta de outras doen\u00E7as que causam dilata\u00E7\u00E3o ductal causada por obstru\u00E7\u00E3o, por n\u00E3o ser um dos muitos derivados do cisto de col\u00E9doco."@pt . "308573"^^ . . . . . . . . . "29874"^^ . . . "radio"@en . . "Choroba Carolego"@pl . . "263200"^^ . . . "\u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A"@ar . . . "Choroba Carolego (ang. Caroli disease) \u2013 to dziedziczne schorzenie wewn\u0105trzw\u0105trobowych dr\u00F3g \u017C\u00F3\u0142ciowych, o typie dziedziczenia najcz\u0119\u015Bciej autosomalnym recesywnym, rzadziej autosomalnym dominuj\u0105cym, przejawiaj\u0105ce si\u0119 powstawaniem poszerze\u0144 (tak zwanych torbieli, kt\u00F3re jednak nie spe\u0142niaj\u0105 kryteri\u00F3w histologicznych rozpoznania torbieli, gdy\u017C nie s\u0105 wys\u0142ane nab\u0142onkiem) dr\u00F3g \u017C\u00F3\u0142ciowych. W jej przebiegu dochodzi do rozwoju nadci\u015Bnienia wrotnego i marsko\u015Bci w\u0105troby."@pl . "Congenital cystic dilatation of the intrahepatic biliar tree"@en . . "Maladie de Caroli"@fr . "Turbo spin echo T2-weighted axial MRI of Caroli disease, showing cystic dilatations of bile ducts ."@en . . . . . . . . "Caroli disease (communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree) is a rare inherited disorder characterized by cystic dilatation (or ectasia) of the bile ducts within the liver. There are two patterns of Caroli disease: focal or simple Caroli disease consists of abnormally widened bile ducts affecting an isolated portion of liver. The second form is more diffuse, and when associated with portal hypertension and congenital hepatic fibrosis, is often referred to as \"Caroli syndrome\". The underlying differences between the two types are not well understood. Caroli disease is also associated with liver failure and polycystic kidney disease. The disease affects about one in 1,000,000 people, with more reported cases of Caroli syndrome than of Ca"@en . . . . . "La maladie de Caroli est une affection cong\u00E9nitale rare du foie. Elle se caract\u00E9rise par des dilatations kystiques des voies biliaires intrah\u00E9patiques ; ces ont une r\u00E9partition segmentaire ce qui rend plus ais\u00E9e une h\u00E9patectomie partielle si elle s'av\u00E8re n\u00E9cessaire."@fr . "La Enfermedad de Caroli (ectasia cavernosa comunicante o dilataci\u00F3n qu\u00EDstica cong\u00E9nita del \u00E1rbol biliar intrahep\u00E1tico ) es un raro desorden hereditario caracterizado por la dilataci\u00F3n de los ductos biliares intrahep\u00E1ticos. Se consideran dos subtipos de enfermedad de Caroli, siendo el m\u00E1s frecuente el llamado simple o aislado y se presenta cuando los ductos biliares se encuentran dilatados por ectasia. El segundo subtipo, m\u00E1s complejo, se conoce com\u00FAnmente como s\u00EDndrome de Caroli. Esta forma compleja se encuentra vinculada a hipertensi\u00F3n portal y .\u200B Las diferencias entre las causales de los dos subtipos todav\u00EDa no han sido bien esclarecidas. La enfermedad de Caroli se encuentra adem\u00E1s asociada a fallo hep\u00E1tico y enfermedad poliqu\u00EDstica renal. Esta enfermedad afecta aproximadamente a 1 en 1.000.000 de pacientes, con un mayor n\u00FAmero de casos reportados de s\u00EDndrome de Caroli que de enfermedad de Caroli en su forma simple.\u200B Esta enfermedad es distinta de otras enfermedades que causan dilataci\u00F3n ductal por obstrucci\u00F3n, y por lo tanto no se la considera una m\u00E1s de las muchas enfermedades derivadas de los quistes de col\u00E9doco.\u200B"@es . . . . . . . "53035" . "131"^^ . "\u0411\u043E\u043B\u0435\u0301\u0437\u043D\u044C \u041A\u0430\u0440\u043E\u043B\u0438\u0301 (\u0441\u0438\u043D\u0434\u0440\u043E\u043C \u041A\u0430\u0440\u043E\u043B\u0438) \u2014 \u0432\u043F\u0435\u0440\u0432\u044B\u0435 \u043E\u043F\u0438\u0441\u0430\u043D\u0430 \u0444\u0440\u0430\u043D\u0446\u0443\u0437\u0441\u043A\u0438\u043C \u0433\u0430\u0441\u0442\u0440\u043E\u044D\u043D\u0442\u0435\u0440\u043E\u043B\u043E\u0433\u043E\u043C \u0416\u0430\u043A\u043E\u043C \u041A\u0430\u0440\u043E\u043B\u0438 \u0432 1958 \u0433\u043E\u0434\u0443, \u044F\u0432\u043B\u044F\u0435\u0442\u0441\u044F \u0440\u0435\u0434\u043A\u0438\u043C \u043D\u0430\u0441\u043B\u0435\u0434\u0441\u0442\u0432\u0435\u043D\u043D\u044B\u043C \u0437\u0430\u0431\u043E\u043B\u0435\u0432\u0430\u043D\u0438\u0435\u043C, \u043A\u043E\u0442\u043E\u0440\u043E\u0435 \u0445\u0430\u0440\u0430\u043A\u0442\u0435\u0440\u0438\u0437\u0443\u0435\u0442\u0441\u044F \u043A\u0438\u0441\u0442\u043E\u0437\u043D\u044B\u043C \u0440\u0430\u0441\u0448\u0438\u0440\u0435\u043D\u0438\u0435\u043C \u0432\u043D\u0443\u0442\u0440\u0438\u043F\u0435\u0447\u0435\u043D\u043E\u0447\u043D\u044B\u0445 \u0436\u0435\u043B\u0447\u043D\u044B\u0445 \u043F\u0440\u043E\u0442\u043E\u043A\u043E\u0432. \u041C\u041A\u0411-10- Q44.5. \u041D\u0430\u0441\u043B\u0435\u0434\u043E\u0432\u0430\u043D\u0438\u0435 \u043F\u043E \u0430\u0443\u0442\u043E\u0441\u043E\u043C\u043D\u043E-\u0440\u0435\u0446\u0435\u0441\u0441\u0438\u0432\u043D\u043E\u043C\u0443 \u0442\u0438\u043F\u0443, \u043C\u0443\u0442\u0430\u0446\u0438\u044F \u0433\u0435\u043D\u0430 PKHD1."@ru . . "Choroba Carolego (ang. Caroli disease) \u2013 to dziedziczne schorzenie wewn\u0105trzw\u0105trobowych dr\u00F3g \u017C\u00F3\u0142ciowych, o typie dziedziczenia najcz\u0119\u015Bciej autosomalnym recesywnym, rzadziej autosomalnym dominuj\u0105cym, przejawiaj\u0105ce si\u0119 powstawaniem poszerze\u0144 (tak zwanych torbieli, kt\u00F3re jednak nie spe\u0142niaj\u0105 kryteri\u00F3w histologicznych rozpoznania torbieli, gdy\u017C nie s\u0105 wys\u0142ane nab\u0142onkiem) dr\u00F3g \u017C\u00F3\u0142ciowych. W jej przebiegu dochodzi do rozwoju nadci\u015Bnienia wrotnego i marsko\u015Bci w\u0105troby."@pl . . . . . . . . . . . . . . . "Das Caroli-Syndrom, benannt nach seinem Erstbeschreiber Jacques Caroli (1902\u20131979), ist eine seltene angeborene Erkrankung der Gallenwege mit zystischen Erweiterungen der Galleng\u00E4nge in Kombination mit einer angeborenen Fibrose der Leber. Die isolierte Erweiterung der gro\u00DFen Gallenwege ohne Bindegewebsvermehrung ist als Caroli-Krankheit bekannt."@de . . . . . . . . . . . . "radio"@en . . . "53035"^^ . . . "Caroli disease"@en . . . . . . . . "Caroli disease"@en . . "D016767"@en . . . . . . . "Doen\u00E7a de Caroli"@pt . . . . . . . "\u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A (\u0628\u0627\u0644\u0625\u0646\u062C\u0644\u064A\u0632\u064A\u0629: Caroli disease)\u200F (\u062A\u0648\u0633\u0639 \u0643\u0647\u0641\u064A \u0645\u062A\u0635\u0644\u060C \u0623\u0648 \u062A\u0648\u0633\u0639 \u0643\u064A\u0633\u064A \u062E\u0644\u0642\u064A \u0644\u0644\u0623\u0642\u0646\u064A\u0629 \u0627\u0644\u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u062F\u0627\u062E\u0644 \u0627\u0644\u0643\u0628\u062F) \u0647\u0648 \u0627\u0636\u0637\u0631\u0627\u0628 \u0648\u0631\u0627\u062B\u064A \u0646\u0627\u062F\u0631 \u064A\u062A\u0645\u064A\u0632 \u0628\u0627\u0644\u062A\u0648\u0633\u0639 \u0627\u0644\u0643\u064A\u0633\u064A\u060C \u0623\u0648 \u062A\u0648\u0633\u0639 \u0627\u0644\u0642\u0646\u0648\u0627\u062A \u0627\u0644\u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u062F\u0627\u062E\u0644 \u0627\u0644\u0643\u0628\u062F. \u064A\u0648\u062C\u062F \u0646\u0645\u0637\u0627\u0646 \u0644\u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A: \u064A\u062A\u0643\u0648\u0646 \u062F\u0627\u0621 \u0643\u0627\u0631\u0648\u0644\u064A \u0627\u0644\u0628\u0624\u0631\u064A \u0623\u0648 \u0645\u0631\u0636 \u0643\u0627\u0631\u0648\u0644\u064A \u0627\u0644\u0628\u0633\u064A\u0637 \u0645\u0646 \u0642\u0646\u0648\u0627\u062A \u0635\u0641\u0631\u0627\u0648\u064A\u0629 \u0645\u062A\u0633\u0639\u0629 \u0628\u0634\u0643\u0644 \u063A\u064A\u0631 \u0637\u0628\u064A\u0639\u064A \u062A\u0624\u062B\u0631 \u0639\u0644\u0649 \u062C\u0632\u0621 \u0645\u0639\u0632\u0648\u0644 \u0645\u0646 \u0627\u0644\u0643\u0628\u062F. \u0627\u0644\u0634\u0643\u0644 \u0627\u0644\u062B\u0627\u0646\u064A \u0623\u0643\u062B\u0631 \u0627\u0646\u062A\u0634\u0627\u0631\u064B\u0627\u060C \u0648\u0639\u0646\u062F\u0645\u0627 \u064A\u0631\u062A\u0628\u0637 \u0628\u0627\u0631\u062A\u0641\u0627\u0639 \u0636\u063A\u0637 \u0627\u0644\u062F\u0645 \u0627\u0644\u0628\u0627\u0628\u064A \u0648\u0627\u0644\u062A\u0644\u064A\u0641 \u0627\u0644\u0643\u0628\u062F\u064A \u0627\u0644\u062E\u0644\u0642\u064A \u063A\u0627\u0644\u0628\u064B\u0627 \u0645\u0627 \u064A\u0634\u0627\u0631 \u0625\u0644\u064A\u0647 \u0628\u0627\u0633\u0645 \u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0643\u0627\u0631\u0648\u0644\u064A. \u0627\u0644\u0627\u062E\u062A\u0644\u0627\u0641\u0627\u062A \u0627\u0644\u0623\u0633\u0627\u0633\u064A\u0629 \u0628\u064A\u0646 \u0627\u0644\u0646\u0648\u0639\u064A\u0646 \u0644\u064A\u0633\u062A \u0645\u0641\u0647\u0648\u0645\u0629 \u062C\u064A\u062F\u064B\u0627. \u064A\u0631\u062A\u0628\u0637 \u062F\u0627\u0621 \u0643\u0627\u0631\u0648\u0644\u064A \u0623\u064A\u0636\u064B\u0627 \u0628\u0641\u0634\u0644 \u0627\u0644\u0643\u0628\u062F \u0648\u062F\u0627\u0621 \u0627\u0644\u0643\u0644\u0649 \u0645\u062A\u0639\u062F\u062F \u0627\u0644\u0643\u064A\u0633\u0627\u062A. \u064A\u0635\u064A\u0628 \u0627\u0644\u0645\u0631\u0636 \u0634\u062E\u0635\u064B\u0627 \u0648\u0627\u062D\u062F\u064B\u0627 \u0645\u0646 \u0628\u064A\u0646 \u0643\u0644 \u0645\u0644\u064A\u0648\u0646 \u0634\u062E\u0635\u060C \u0645\u0639 \u0648\u062C\u0648\u062F \u062D\u0627\u0644\u0627\u062A \u0625\u0635\u0627\u0628\u0629 \u0628\u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0643\u0627\u0631\u0648\u0644\u064A \u0623\u0643\u062B\u0631 \u0645\u0646 \u0627\u0644\u0645\u0631\u0636."@ar . . . . . "1118763891"^^ . . . . . . . . . . "Malattia di Caroli"@it . . . "La malattia di Caroli \u00E8 una patologia congenita che si caratterizza per la presenza di cisti dei dotti biliari intraepatici. Quest'evento sembra essere legato alla dilatazione segmentale e multifocale, ma non si conosce l'evento scatenante, esordisce in qualunque et\u00E0 con prevalenza nel sesso femminile e con carattere ereditario autosomico recessivo. \u00C8 una malattia molto rara e ad oggi sono stati descritti meno di trecento casi in tutto il mondo. Oltre alla dilatazione delle vie intraepatiche non sussistono altre alterazioni."@it . . . . . . "\u0411\u043E\u043B\u0435\u0301\u0437\u043D\u044C \u041A\u0430\u0440\u043E\u043B\u0438\u0301 (\u0441\u0438\u043D\u0434\u0440\u043E\u043C \u041A\u0430\u0440\u043E\u043B\u0438) \u2014 \u0432\u043F\u0435\u0440\u0432\u044B\u0435 \u043E\u043F\u0438\u0441\u0430\u043D\u0430 \u0444\u0440\u0430\u043D\u0446\u0443\u0437\u0441\u043A\u0438\u043C \u0433\u0430\u0441\u0442\u0440\u043E\u044D\u043D\u0442\u0435\u0440\u043E\u043B\u043E\u0433\u043E\u043C \u0416\u0430\u043A\u043E\u043C \u041A\u0430\u0440\u043E\u043B\u0438 \u0432 1958 \u0433\u043E\u0434\u0443, \u044F\u0432\u043B\u044F\u0435\u0442\u0441\u044F \u0440\u0435\u0434\u043A\u0438\u043C \u043D\u0430\u0441\u043B\u0435\u0434\u0441\u0442\u0432\u0435\u043D\u043D\u044B\u043C \u0437\u0430\u0431\u043E\u043B\u0435\u0432\u0430\u043D\u0438\u0435\u043C, \u043A\u043E\u0442\u043E\u0440\u043E\u0435 \u0445\u0430\u0440\u0430\u043A\u0442\u0435\u0440\u0438\u0437\u0443\u0435\u0442\u0441\u044F \u043A\u0438\u0441\u0442\u043E\u0437\u043D\u044B\u043C \u0440\u0430\u0441\u0448\u0438\u0440\u0435\u043D\u0438\u0435\u043C \u0432\u043D\u0443\u0442\u0440\u0438\u043F\u0435\u0447\u0435\u043D\u043E\u0447\u043D\u044B\u0445 \u0436\u0435\u043B\u0447\u043D\u044B\u0445 \u043F\u0440\u043E\u0442\u043E\u043A\u043E\u0432. \u041C\u041A\u0411-10- Q44.5. \u041D\u0430\u0441\u043B\u0435\u0434\u043E\u0432\u0430\u043D\u0438\u0435 \u043F\u043E \u0430\u0443\u0442\u043E\u0441\u043E\u043C\u043D\u043E-\u0440\u0435\u0446\u0435\u0441\u0441\u0438\u0432\u043D\u043E\u043C\u0443 \u0442\u0438\u043F\u0443, \u043C\u0443\u0442\u0430\u0446\u0438\u044F \u0433\u0435\u043D\u0430 PKHD1."@ru . . . . . . "Caroli-Syndrom"@de . . . . . . "La maladie de Caroli est une affection cong\u00E9nitale rare du foie. Elle se caract\u00E9rise par des dilatations kystiques des voies biliaires intrah\u00E9patiques ; ces ont une r\u00E9partition segmentaire ce qui rend plus ais\u00E9e une h\u00E9patectomie partielle si elle s'av\u00E8re n\u00E9cessaire."@fr . . . . .